A Case of Mccune- Albright Syndrome
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Abstract:
Four year old girl was evaluated for precocious puberty. Breast development and pubic hair growth had started at age 2½ year, and had been followed by vaginal bleeding resembling periods. Gaf-au-lait spots were present in most of her skin surface. Bone x-rays showed multiple cysts in pelvis and the metaphysis of femur. Diagnosis of McCune-Albright syndrome was made. Concentrations of all hormones were within normal limits. Treatment with medroxyprogesterone and cyproterone acetate, in separate occasions, was successful.
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full textmccune-albright syndrome: report of a case
a 29- year old female with bone pain and history of precocious puberty was referred for bone scintigraphy. on physical examination café au lait macular spots were noted on her neck, buttocks and left leg. bone scan showed multiple areas of intense increased activity which was in favour of polyostotic fibrous dysplasia. considering the presence of polyostotic fibrous dysplasia, precocious pubert...
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Journal title
volume 12 issue 1
pages 51- 56
publication date 1988-03
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